ICD-10 Code E76.9 – Glucosaminoglycan Metabolism Disorder, Unspecified (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E76.9 – Glucosaminoglycan metabolism disorder, unspecified
What it is
E76.9 identifies an unspecified disorder of glycosaminoglycan metabolism, a group of inherited conditions that affect how the body breaks down certain complex sugars. Use this code when the record confirms the disorder but does not name a specific type.
Clinical signs
Clinical features vary; refer to documentation. Standard references describe possible skeletal changes, developmental delay, organ enlargement, or other findings associated with mucopolysaccharide storage disorders.
When to use this code
Use E76.9 when the provider documents a glycosaminoglycan metabolism disorder but does not specify the subtype. It also fits when the chart confirms a related inherited storage disorder and the exact diagnosis is still pending. Check documentation if the record names a more specific condition.
Do not use for
Do not use this code when the chart identifies a specific glycosaminoglycan metabolism disorder, such as a named mucopolysaccharidosis. Also avoid it if the documentation only suggests a suspected disorder without confirmation.
Coding tip
Always code to the most specific documented diagnosis; use E76.9 only when the provider leaves the disorder unspecified.