ICD-10 Code E71.529 – X-linked adrenoleukodystrophy, unspecified type (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E71.529 – X-linked adrenoleukodystrophy, unspecified type
What it is
E71.529 identifies X-linked adrenoleukodystrophy when the record does not specify a cerebral, adrenal, or other subtype. It is a hereditary peroxisomal disorder that affects very long-chain fatty acid metabolism.
Clinical signs
Clinical features vary; refer to documentation. Commonly documented findings include progressive neurologic decline, gait problems, and adrenal insufficiency, but you should code only what is supported in the chart.
When to use this code
Use this code when the provider documents X-linked adrenoleukodystrophy without naming a specific type. It also fits cases where the diagnosis is confirmed, but the subtype is not stated in the assessment or problem list. If the note names a more specific form, you should code that instead.
Do not use for
Do not use this code for a different leukodystrophy, nonspecific adrenal disorder, or a carrier state without disease. Check documentation if the record only mentions family history or suspected disease.
Coding tip
Look for the exact wording “unspecified type” or an equivalent omission before assigning E71.529.