ICD-10 Code E71.522 – Adrenomyeloneuropathy (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E71.522 – Adrenomyeloneuropathy
What it is
Adrenomyeloneuropathy is a hereditary disorder that affects the spinal cord and peripheral nerves, often as part of the X-linked adrenoleukodystrophy spectrum. Use this code for the documented diagnosis, not for nonspecific weakness alone.
Clinical signs
Typical findings include progressive spastic paraparesis, gait difficulty, sensory changes, and bladder symptoms. Clinical features vary; refer to documentation for neurologic involvement and any confirmed adrenal disease.
When to use this code
Use E71.522 when the clinician documents adrenomyeloneuropathy specifically, including evaluations that confirm the diagnosis. It also fits follow-up visits for a known case, even if the current note focuses on monitoring or chronic management. Check documentation if the record only says leukodystrophy, myelopathy, or neuropathy without this exact diagnosis.
Do not use for
Do not use this code for isolated peripheral neuropathy, spinal cord disease, or adrenal insufficiency without documented adrenomyeloneuropathy. If the diagnosis is uncertain or broader, check documentation.
Coding tip
Code the specific documented disorder and confirm whether the note identifies the adrenomyeloneuropathy subtype rather than a general leukodystrophy code.