ICD-10 Code E71.32 – Disorders of ketone metabolism (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E71.32 – Disorders of ketone metabolism
What it is
This code identifies a disorder affecting the body’s normal handling of ketones, which are energy substances made from fat. Use it when documentation states a ketone metabolism disorder without a more specific named diagnosis.
Clinical signs
Clinical features vary; refer to documentation. Patients may have recurrent metabolic decompensation, ketosis-related symptoms, or abnormal ketone handling noted by the clinician.
When to use this code
Use E71.32 when the provider documents a disorder of ketone metabolism, ketolysis defect, or another ketone-related metabolic condition and no more specific code is available. It is appropriate for confirmed diagnoses in the medical record, not for suspected metabolic problems.
Do not use for
Do not use this code for diabetic ketoacidosis, simple ketosis, or conditions where ketone findings are incidental. Check documentation if the record names a different inborn error of metabolism or a more specific diagnosis.
Coding tip
Confirm the exact metabolic diagnosis in the chart before coding, because ketone-related terms are sometimes used loosely.