ICD-10 Code E71.312 – Short chain acyl CoA dehydrogenase deficiency (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E71.312 – Short chain acyl CoA dehydrogenase deficiency
What it is
E71.312 identifies short-chain acyl-CoA dehydrogenase deficiency, an inherited disorder of fatty acid metabolism. It means the body has trouble breaking down certain fats for energy.
Clinical signs
Clinical features vary; refer to documentation. Commonly reported findings include episodes of hypoglycemia, poor feeding, vomiting, lethargy, and metabolic decompensation, especially during fasting or illness.
When to use this code
Use this code when the record specifically documents short-chain acyl-CoA dehydrogenase deficiency or SCADD. Apply it for confirmed diagnoses, genetic or metabolic workups, or specialist assessments that identify this condition. Do not code it from nonspecific abnormal screening alone.
Do not use for
Do not use E71.312 for other fatty acid oxidation disorders, acyl-CoA dehydrogenase deficiencies of different chain lengths, or an undiagnosed metabolic disorder. Check documentation if the chart only says “possible” or “rule out.”
Coding tip
Code only when the provider documents the disorder explicitly; if the record is unclear, query for confirmation before assigning E71.312.