ICD-10 Code D69.41 – Evans syndrome (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code D69.41 – Evans syndrome
What it is
Evans syndrome is an autoimmune disorder in which the body destroys its own red blood cells and platelets. Use this code for the documented syndrome, not for isolated anemia or thrombocytopenia.
Clinical signs
Typical findings include signs of hemolytic anemia and low platelet counts, such as fatigue, pallor, jaundice, bruising, or bleeding. Clinical features vary; refer to documentation.
When to use this code
Use D69.41 when the provider documents Evans syndrome explicitly or clearly identifies autoimmune hemolytic anemia with immune thrombocytopenia as the syndrome. It is appropriate when the diagnosis is established in the record, even if current symptoms are not detailed.
Do not use for
Do not use this code for anemia alone, thrombocytopenia alone, or other non-autoimmune causes of cytopenias. Check documentation if the record does not clearly state Evans syndrome.
Coding tip
Code Evans syndrome only when the diagnosis is stated or supported by clear provider documentation.