ICD-10 Code D68.03 – Von Willebrand disease, type 3 (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code D68.03 – Von Willebrand disease, type 3
What it is
Von Willebrand disease, type 3 is the most severe form of this inherited bleeding disorder. It reflects a marked deficiency of von Willebrand factor, which impairs normal clotting and platelet adhesion.
Clinical signs
Patients may have frequent mucocutaneous bleeding, easy bruising, prolonged bleeding after injury, and heavy menstrual bleeding. Clinical features vary; refer to documentation.
When to use this code
Use this code when the record clearly documents type 3 von Willebrand disease or congenital von Willebrand factor deficiency of this subtype. Apply it for confirmed diagnoses in outpatient, inpatient, or historical problem-list coding when the subtype is specified. Check documentation if the subtype is unclear.
Do not use for
Do not use this code for other von Willebrand disease types or for unspecified bleeding disorders. If the note only says “von Willebrand disease” without a subtype, code the documented unspecified form instead.
Coding tip
Always verify the subtype in the assessment, genetics, or hematology note before selecting D68.03.