ICD-10 Code D68.021 – Von Willebrand disease, type 2B (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code D68.021 – Von Willebrand disease, type 2B
What it is
D68.021 identifies type 2B von Willebrand disease, an inherited bleeding disorder caused by an abnormal von Willebrand factor that binds platelets too readily. This code tells you the specific subtype, not just a general bleeding tendency.
Clinical signs
Clinical features vary; refer to documentation. Commonly documented findings include mucocutaneous bleeding such as easy bruising, nosebleeds, gum bleeding, and prolonged bleeding after injury or procedures.
When to use this code
Use this code when the provider documents von Willebrand disease, type 2B, or confirms this subtype in the assessment. It is appropriate for inherited bleeding disorder workups, hematology follow-up, and pre-procedure documentation when the diagnosis is established. Check documentation if the subtype is unclear.
Do not use for
Do not use this code for other von Willebrand disease types, acquired von Willebrand syndrome, or unspecified bleeding disorders. If the record only says “von Willebrand disease” without a subtype, check documentation.
Coding tip
Code the exact subtype only when the provider clearly documents type 2B; otherwise, report the unspecified or more general diagnosis supported by the record.