ICD-10 Code C91.A0 – Mature B-cell leukemia Burkitt-type not having achieved remission (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code C91.A0 – Mature B-cell leukemia Burkitt-type not having achieved remission
What it is
This code identifies Burkitt-type mature B-cell leukemia that has not achieved remission. Use it when documentation states the disease is active, persistent, or not in remission.
Clinical signs
Clinical features vary; refer to documentation. Burkitt-type leukemia may present with rapidly progressive marrow involvement, cytopenias, enlarged lymph nodes, or systemic symptoms, but you should code only what is documented.
When to use this code
Use C91.A0 when the provider documents mature B-cell leukemia, Burkitt-type, and states the patient has not achieved remission. It also fits follow-up notes that confirm active disease after treatment or persistent leukemia. If remission status is unclear, check documentation before assigning the code.
Do not use for
Do not use this code for Burkitt lymphoma, other mature B-cell neoplasms, or leukemia documented as in remission. If the record does not specify Burkitt-type or remission status, check documentation.
Coding tip
Always verify both the subtype and remission status in the provider note before coding.