ICD-10 Code C91.A – Mature B-cell leukemia Burkitt-type (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code C91.A – Mature B-cell leukemia Burkitt-type
What it is
C91.A identifies mature B-cell leukemia, Burkitt-type, a rare aggressive B-cell neoplasm. Use it when the record specifically documents Burkitt-type leukemia rather than lymphoma or another mature B-cell disorder.
Clinical signs
Clinical features vary; refer to documentation. Commonly, records describe a rapidly progressive mature B-cell malignancy with leukemic involvement, and pathology or hematology notes should confirm the Burkitt-type designation.
When to use this code
Use this code when the clinician documents mature B-cell leukemia, Burkitt-type, in the diagnosis or assessment. It is appropriate for confirmed cases in inpatient, outpatient, or problem-list documentation when the wording matches the code description.
If the chart only says Burkitt lymphoma, mature B-cell lymphoma, or another B-cell neoplasm, check documentation before coding C91.A. Code the condition exactly as documented and avoid assuming leukemia involvement without support.
Do not use for
Do not use this code for Burkitt lymphoma without leukemia terminology, or for unspecified mature B-cell neoplasms. Check documentation if the record does not clearly state Burkitt-type leukemia.
Coding tip
Match the exact hematology wording; if the source note is ambiguous, query for whether the diagnosis is leukemia, lymphoma, or both.