ICD-10 Code C75.5 – Malignant neoplasm of aortic body and other paraganglia (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code C75.5 – Malignant neoplasm of aortic body and other paraganglia
What it is
This code identifies a malignant tumor arising from the aortic body or other paraganglial tissue. These are rare neuroendocrine cancers, and you should use the code when documentation specifies malignancy at these sites.
Clinical signs
Clinical features vary; refer to documentation. Patients may present with a mass, local compressive symptoms, or findings related to hormone secretion when the tumor is functional.
When to use this code
Use C75.5 when the provider documents malignant neoplasm of the aortic body or another paraganglion. It also applies when the record clearly states a malignant paraganglioma at one of these sites. If the exact site or malignant nature is unclear, check documentation before coding.
Do not use for
Do not use this code for benign paraganglioma, unspecified paraganglioma, or tumors documented at other endocrine sites. If the record describes a mass without confirmed malignancy, use the more specific documented diagnosis.
Coding tip
Confirm both the malignant behavior and the anatomic site in the provider note before assigning C75.5.