ICD-10 Code A50.49 – Other late congenital neurosyphilis (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code A50.49 – Other late congenital neurosyphilis
What it is
This code identifies late congenital neurosyphilis that does not fit a more specific category. It refers to neurologic disease caused by congenital syphilis recognized later in life.
Clinical signs
Clinical features vary; refer to documentation. Findings may include neurologic, ocular, or auditory abnormalities consistent with late congenital syphilis, but the record should support the diagnosis.
When to use this code
Use A50.49 when the provider documents other late congenital neurosyphilis and no more specific congenital syphilis code applies. Code it for confirmed late manifestations linked to congenital infection, not for screening or exposure alone.
If the note only states suspected syphilis, historical maternal infection, or nonspecific neurologic symptoms, check documentation before assigning this code. The diagnosis should be clearly established in the medical record.
Do not use for
Do not use this code for acquired neurosyphilis, early congenital syphilis, or congenital syphilis without neurologic involvement. Check documentation if the record is unclear.
Coding tip
Confirm that the chart explicitly links the neurologic condition to late congenital syphilis before coding A50.49.