ICD-10 Code A50.04 – Early congenital syphilitic pneumonia (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code A50.04 – Early congenital syphilitic pneumonia
What it is
This code identifies pneumonia occurring in an infant with early congenital syphilis. Use it when the record links respiratory disease to congenital syphilitic infection.
Clinical signs
Clinical features vary; refer to documentation. Reported findings may include respiratory distress, cough, and diffuse lung involvement in a newborn or young infant with congenital syphilis.
When to use this code
Use A50.04 when the provider documents early congenital syphilitic pneumonia or clearly attributes pneumonia to congenital syphilis. It is appropriate for neonatal or infant encounters where the infection is present at birth or diagnosed soon after. Check documentation if the relationship is not explicit.
Do not use for
Do not use this code for pneumonia without congenital syphilis, or for later manifestations of syphilis in childhood. If the chart does not support congenital infection, choose a different pneumonia or syphilis code.
Coding tip
Confirm that both congenital syphilis and pneumonia are documented together before assigning A50.04.