ICD-10 Code A50.3 – Late congenital syphilitic oculopathy (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code A50.3 – Late congenital syphilitic oculopathy
What it is
This code identifies late eye disease caused by congenital syphilis. Use it when documentation shows ocular damage appearing after birth from a congenital syphilis infection.
Clinical signs
Clinical features vary; refer to documentation. Standard references describe interstitial keratitis, chorioretinitis, optic nerve involvement, or other late ocular findings linked to congenital syphilis.
When to use this code
Use A50.3 when the record specifically states late congenital syphilitic eye disease or a related late ocular manifestation due to congenital syphilis. You should code it when the provider links the eye condition to congenital infection, even if the current visit is for evaluation or follow-up.
Do not use for
Do not use this code for acquired syphilis, unspecified congenital syphilis, or eye disease without a documented congenital syphilis cause. Check documentation if the ocular finding is nonspecific.
Coding tip
Confirm that the provider documents both congenital syphilis and the late ocular complication before assigning A50.3.