ICD-10 Code E71.311 – Medium chain acyl CoA dehydrogenase deficiency (2026): Diagnosis, Symptoms & Billing Guide
The ICD-10 code for Medium chain acyl CoA dehydrogenase deficiency is E71.311.2026 ICD-10-CM Diagnosis Code E71.311 – Medium chain acyl CoA dehydrogenase deficiency Related ICD-10 Codes Parent code: E71 – Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism Other codes in same category: E71.0 – Maple-syrup-urine disease, E71.1 – Other disorders of branched-chain amino-acid metabolism,…