ICD-10 Code G71.0340 – Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G71.0340 – Limb girdle muscular dystrophy due to sarcoglycan dysfunction, unspecified
What it is
This code identifies a limb-girdle muscular dystrophy caused by sarcoglycan dysfunction when the specific subtype is not documented. It refers to an inherited muscle disorder that mainly affects the shoulder and pelvic girdle muscles.
Clinical signs
Typical findings include progressive proximal muscle weakness, difficulty climbing stairs, rising from a chair, or lifting the arms. Clinical features vary; refer to documentation for the exact sarcoglycan-related diagnosis.
When to use this code
Use this code when the record states limb-girdle muscular dystrophy due to sarcoglycan dysfunction but does not name the specific gene or subtype. You may also use it when the provider documents sarcoglycan-related LGMD as unspecified. Check documentation if the chart names a more specific dystrophy type.
Do not use for
Do not use this code for other muscular dystrophies, acquired myopathies, or generalized weakness without a documented sarcoglycan cause. If the subtype is specified elsewhere, code the more precise diagnosis.
Coding tip
Query the provider when the note says “LGMD” but does not clearly link it to sarcoglycan dysfunction.