ICD-10 Code E80.2 – Other and unspecified porphyria (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E80.2 – Other and unspecified porphyria
What it is
E80.2 identifies porphyria that is not classified as a specific inherited type. It covers cases where the record documents porphyria, but the subtype is other or not further specified.
Clinical signs
Clinical features vary; refer to documentation. Porphyria may present with abdominal pain, neurologic symptoms, skin findings, or dark urine, depending on the subtype and whether the condition is acute or cutaneous.
When to use this code
Use E80.2 when the provider documents other porphyria or unspecified porphyria and does not name a more specific type. It is also appropriate when the chart confirms porphyria, but the subtype is not available in the note, problem list, or test results.
Do not assume a specific porphyria subtype from symptoms alone. If the documentation is incomplete, code only what is clearly stated and query when a more precise diagnosis may be supported.
Do not use for
Do not use this code for a documented specific porphyria type when a more exact ICD-10-CM code exists. Also avoid it if porphyria is only suspected, ruled out, or not confirmed in the record.
Coding tip
Check the provider’s exact wording for “other,” “unspecified,” or a named porphyria subtype before assigning E80.2.