ICD-10 Code E74.11 – Essential fructosuria (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E74.11 – Essential fructosuria
What it is
Essential fructosuria is an inherited carbohydrate metabolism condition in which the body cannot properly process fructose. It is usually benign and often found incidentally.
Clinical signs
Clinical features vary; refer to documentation. Many patients have no symptoms, but fructose may appear in the urine after ingestion, and mild gastrointestinal or metabolic concerns may prompt evaluation.
When to use this code
Use this code when the provider documents essential fructosuria, fructokinase deficiency, or a confirmed inherited fructose metabolism disorder. It applies when the diagnosis is established and not just suspected. Check documentation if the record only notes fructose intolerance or another metabolic problem.
Do not use for
Do not use this code for hereditary fructose intolerance, which is a different and more serious disorder. Also avoid it when the chart only mentions nonspecific fructose sensitivity or an unconfirmed abnormal urine finding.
Coding tip
Code only when the provider clearly identifies essential fructosuria; otherwise, verify whether a different fructose disorder is documented.