ICD-10 Code E74.0 – Glycogen storage disease (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E74.0 – Glycogen storage disease
What it is
E74.0 identifies glycogen storage disease, a group of inherited metabolic disorders in which the body cannot properly store or break down glycogen. The result is abnormal glycogen accumulation or impaired glucose release.
Clinical signs
Clinical features vary by subtype and may include hepatomegaly, muscle weakness, exercise intolerance, or recurrent hypoglycemia. Check documentation for the specific type and whether the diagnosis is confirmed.
When to use this code
Use E74.0 when the provider documents glycogen storage disease without naming a more specific subtype, or when the record only states the broader disorder. It also fits follow-up visits for a confirmed diagnosis already established in the chart.
If the note identifies a specific glycogen storage disease type, code that more precise diagnosis instead. Review the assessment carefully and code from the documented type, not from presumed symptoms.
Do not use for
Do not use E74.0 for hypoglycemia alone, liver disease without a glycogen storage diagnosis, or other inherited carbohydrate disorders. Clinical features vary; refer to documentation.
Coding tip
Look for the exact subtype name in the assessment, because a more specific ICD-10-CM code may apply.