ICD-10 Code E71.318 – Other disorders of fatty-acid oxidation (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E71.318 – Other disorders of fatty-acid oxidation
What it is
E71.318 identifies inherited disorders that impair the body’s ability to break down fatty acids for energy. Use it when documentation names a fatty-acid oxidation disorder that is not more specifically classified elsewhere.
Clinical signs
Clinical features vary; refer to documentation. Commonly reported findings include recurrent hypoglycemia, lethargy, vomiting, muscle weakness, or episodes triggered by fasting or illness.
When to use this code
Use this code when the provider documents a specific fatty-acid oxidation disorder and the record does not support a more precise code. It may also fit when the condition is described as “other” or “unspecified” fatty-acid oxidation disorder. Check documentation for the exact diagnosis name and any inherited metabolic disorder terminology.
Do not use for
Do not use it for general hypoglycemia, malnutrition, or other metabolic disorders without documentation of fatty-acid oxidation impairment. If a more specific fatty-acid oxidation diagnosis is documented, code that instead.
Coding tip
Match the code to the provider’s exact wording and verify whether a more specific inherited metabolic disorder code applies.