ICD-10 Code A50 – Congenital Syphilis (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code A50 – Congenital syphilis
What it is
A50 identifies congenital syphilis, an infection caused by Treponema pallidum that is present in a newborn or child because it was passed from the mother during pregnancy or delivery.
Clinical signs
Clinical features vary; refer to documentation. Findings may include rash, hepatosplenomegaly, snuffles, bone changes, jaundice, anemia, or later stigmata if untreated.
When to use this code
Use A50 when the record documents congenital syphilis or a confirmed congenital treponemal infection in the infant or child. It also fits cases described as early or late congenital disease when the provider does not assign a more specific subcode. If the chart only notes maternal syphilis exposure without infant infection, check documentation.
Do not use for
Do not use A50 for acquired syphilis in adolescents or adults, or for maternal syphilis alone. If documentation is nonspecific and does not confirm congenital infection, check documentation.
Coding tip
Match the code to provider wording carefully, and look for whether the record identifies congenital infection, specific stage, or only exposure.