ICD-10 Code I28.0 – Arteriovenous fistula of pulmonary vessels (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code I28.0 – Arteriovenous fistula of pulmonary vessels
What it is
I28.0 identifies an abnormal direct connection between a pulmonary artery and a pulmonary vein. This vascular shunt bypasses the normal capillary bed and can alter blood flow through the lungs.
Clinical signs
Clinical features vary; refer to documentation. Patients may have signs related to impaired oxygenation or an incidental imaging finding showing a pulmonary vascular malformation or fistulous connection.
When to use this code
Use this code when the record specifically documents an arteriovenous fistula involving pulmonary vessels. It may appear in radiology, pulmonology, or cardiothoracic documentation describing a congenital or acquired pulmonary vascular shunt. Check documentation if the note only mentions a general vascular anomaly.
Do not use for
Do not use it for a fistula in another body site or for nonspecific pulmonary vascular disease. If the chart does not clearly identify pulmonary vessels, check documentation.
Coding tip
Assign I28.0 only when the provider links the fistula to pulmonary vessels, not when the finding is merely suspected or incidental without confirmation.