ICD-10 Code D58.1 – Hereditary elliptocytosis (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code D58.1 – Hereditary elliptocytosis
What it is
D58.1 identifies hereditary elliptocytosis, an inherited red blood cell membrane disorder that causes elliptically shaped erythrocytes. It is used when documentation states this specific diagnosis.
Clinical signs
Findings may include elliptocytes on peripheral smear, mild hemolysis, jaundice, anemia, or splenomegaly. Clinical features vary; refer to documentation.
When to use this code
Use D58.1 when the provider documents hereditary elliptocytosis, including confirmed cases and follow-up visits for the condition. Code it when the record identifies the inherited membrane defect rather than a nonspecific anemia alone.
If the chart describes elliptocytes without a hereditary diagnosis, check documentation before assigning this code. Make sure the diagnosis is current and not listed only as a historical finding.
Do not use for
Do not use D58.1 for acquired poikilocytosis, iron deficiency anemia, or other hemolytic disorders without hereditary elliptocytosis. Check documentation if the cause is unclear.
Coding tip
Code the specific inherited diagnosis only when the provider documents it; otherwise, query for clarification.