ICD-10 Code C46 – Kaposi’s sarcoma (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code C46 – Kaposi’s sarcoma
What it is
C46 identifies Kaposi’s sarcoma, a malignant vascular tumor that can involve skin, mucous membranes, lymph nodes, or internal organs. Use this code when the diagnosis is documented as Kaposi’s sarcoma.
Clinical signs
Typical findings include violaceous, red, or brown skin or mucosal lesions that may be flat, raised, or nodular. Clinical features vary; refer to documentation for site and extent.
When to use this code
Use C46 when the provider documents Kaposi’s sarcoma as the confirmed diagnosis, whether it is cutaneous, oral, or systemic. You may also code it when pathology or specialist notes clearly identify the condition. If the record only says “suspected” or “rule out,” check documentation.
Do not use for
Do not use C46 for benign vascular lesions, nonspecific skin discoloration, or other tumors that are not documented as Kaposi’s sarcoma. Do not assume the diagnosis from HIV status alone.
Coding tip
Code the documented anatomic site and any stated extent or involvement; if the record is unclear, query for clarification.