ICD-10 Code J84.83 – Surfactant mutations of the lung (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code J84.83 – Surfactant mutations of the lung
What it is
J84.83 identifies surfactant mutations of the lung, a rare inherited disorder affecting the lung surfactant system. Use it when documentation specifically links the condition to a surfactant-related genetic abnormality.
Clinical signs
Clinical features vary; refer to documentation. Common references describe respiratory distress, chronic interstitial lung disease, or diffuse lung disease, especially when symptoms begin in infancy or childhood.
When to use this code
Use this code when the provider documents surfactant mutation, surfactant protein disorder, or a confirmed genetic surfactant abnormality involving the lung. It is also appropriate when the record clearly states a surfactant-related interstitial lung disease diagnosis. Check documentation if the genetic cause is not specified.
Do not use for
Do not use this code for nonspecific interstitial lung disease, pneumonia, or respiratory distress without a documented surfactant mutation. If the chart only mentions suspected genetic lung disease, check documentation.
Coding tip
Code J84.83 only when the record supports a surfactant mutation as the cause, and verify any associated genetic test or specialist note.