ICD-10 Code I00 – Rheumatic fever without heart involvement (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code I00 – Rheumatic fever without heart involvement
What it is
I00 identifies acute rheumatic fever when the heart is not involved. Use it for rheumatic fever manifestations without evidence of carditis or rheumatic heart disease.
Clinical signs
Clinical features may include migratory joint inflammation, fever, or other post-streptococcal rheumatic findings. Clinical features vary; refer to documentation.
When to use this code
Use I00 when the provider documents rheumatic fever and specifically states there is no heart involvement. It may apply during an acute episode after streptococcal infection when cardiac findings are absent. If the record suggests carditis, do not use this code.
Do not use for
Do not use I00 for rheumatic fever with carditis, rheumatic heart disease, or other cardiac complications. Check documentation if the chart does not clearly exclude heart involvement.
Coding tip
Confirm the note explicitly says “without heart involvement” before assigning I00.