ICD-10 Code I01 – Rheumatic fever with heart involvement (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code I01 – Rheumatic fever with heart involvement
What it is
I01 identifies rheumatic fever when the heart is affected. Use it for acute rheumatic carditis or rheumatic heart involvement linked to a recent streptococcal infection.
Clinical signs
Findings may include carditis, new or changing heart murmurs, tachycardia, chest discomfort, or signs of heart failure. Clinical features vary; refer to documentation.
When to use this code
Use I01 when the record clearly documents rheumatic fever with cardiac involvement, including rheumatic carditis or rheumatic heart disease from an acute episode. It is appropriate when the provider links the heart findings to rheumatic fever. If the documentation only says “history of rheumatic fever” without current cardiac involvement, check documentation.
Do not use for
Do not use this code for non-rheumatic myocarditis, endocarditis, or chronic heart disease without an active rheumatic fever diagnosis. Do not code it from suspicion alone.
Coding tip
Confirm that the provider explicitly connects the cardiac condition to rheumatic fever before assigning I01.