ICD-10 Code L90.4 – Acrodermatitis chronica atrophicans (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code L90.4 – Acrodermatitis chronica atrophicans
What it is
L90.4 identifies acrodermatitis chronica atrophicans, a chronic skin disorder that causes progressive thinning and discoloration of the skin. It is usually documented as a late manifestation of Lyme disease.
Clinical signs
Typical findings include persistent bluish-red or violaceous skin changes, swelling, and gradual atrophy, often on the extremities. Clinical features vary; refer to documentation.
When to use this code
Use L90.4 when the record specifically documents acrodermatitis chronica atrophicans or late cutaneous atrophy linked to this condition. Code it when the clinician identifies the disorder by name, even if the note also mentions prior Lyme disease. If the documentation is unclear, check documentation.
Do not use for
Do not use this code for generic dermatitis, cellulitis, or skin atrophy without this diagnosis. Do not assign it when the chart only says Lyme disease without the characteristic skin condition.
Coding tip
Confirm the exact diagnosis wording and document any link to Lyme disease only when the provider states it.