ICD-10 Code L44.0 – Pityriasis rubra pilaris (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code L44.0 – Pityriasis rubra pilaris
What it is
L44.0 identifies pityriasis rubra pilaris, an uncommon inflammatory skin disorder. It is used when the diagnosis is documented and you need to code the condition accurately.
Clinical signs
Typical findings include reddish-orange scaly plaques, follicular papules, and palmoplantar thickening. Clinical features vary; refer to documentation.
When to use this code
Use L44.0 when the provider documents pityriasis rubra pilaris as the confirmed diagnosis. It may also apply when the note clearly describes the condition and supports the diagnosis. If the record is vague, check documentation before assigning the code.
Do not use for
Do not use this code for nonspecific rash, psoriasis, eczema, or other dermatitis unless the provider states pityriasis rubra pilaris. Check documentation when the diagnosis is uncertain.
Coding tip
Code L44.0 only when the chart supports pityriasis rubra pilaris, not just scaling or erythema alone.