ICD-10 Code L41.0 – Pityriasis lichenoides et varioliformis acuta (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code L41.0 – Pityriasis lichenoides et varioliformis acuta
What it is
L41.0 identifies the acute form of pityriasis lichenoides, a rare inflammatory skin disorder. Use it when documentation specifically names pityriasis lichenoides et varioliformis acuta, often abbreviated PLEVA.
Clinical signs
Typical findings include sudden crops of small red-brown papules that may become crusted, necrotic, or varioliform. Clinical features vary; refer to documentation if the record does not clearly describe the rash pattern.
When to use this code
Use this code when the clinician documents PLEVA, acute pityriasis lichenoides, or an equivalent diagnosis in the assessment. It is appropriate for encounters focused on this specific inflammatory eruption, even if the note also mentions pruritus or skin lesions. Check documentation if the wording is nonspecific.
Do not use for
Do not use L41.0 for pityriasis rosea, psoriasis, or other papulosquamous eruptions unless the provider clearly documents PLEVA. If the diagnosis is uncertain or only “rash” is recorded, check documentation.
Coding tip
Code the exact documented form; “pityriasis lichenoides” alone may need clarification before you assign L41.0.