ICD-10 Code K83.01 – Primary sclerosing cholangitis (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code K83.01 – Primary sclerosing cholangitis
What it is
Primary sclerosing cholangitis is a chronic liver disease that causes inflammation and scarring of the bile ducts. The narrowing can block bile flow and gradually damage the liver.
Clinical signs
Clinical features vary; refer to documentation. Common findings include cholestatic liver disease, pruritus, fatigue, and imaging evidence of multifocal bile duct strictures.
When to use this code
Use K83.01 when the provider documents primary sclerosing cholangitis as the confirmed diagnosis. Code it for encounters focused on evaluation, monitoring, or management of this chronic bile duct disorder.
Use the code when records show PSC with or without associated inflammatory bowel disease, as long as PSC is clearly documented. Check documentation if the note only mentions abnormal liver tests or nonspecific cholangitis.
Do not use for
Do not use this code for secondary sclerosing cholangitis, acute cholangitis, or biliary obstruction without PSC. Check documentation if the diagnosis is uncertain or only suspected.
Coding tip
Verify that the provider names primary sclerosing cholangitis explicitly; imaging or biopsy support the code, but the diagnosis must be documented.