ICD-10 Code K74.3 – Primary biliary cirrhosis (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code K74.3 – Primary biliary cirrhosis
What it is
K74.3 identifies primary biliary cirrhosis, now commonly called primary biliary cholangitis. It refers to a chronic autoimmune disease that slowly damages the small bile ducts in the liver.
Clinical signs
Clinical features vary; refer to documentation. Commonly documented findings include chronic cholestatic liver disease, pruritus, fatigue, and evidence of bile duct injury or cirrhosis on evaluation.
When to use this code
Use K74.3 when the provider documents primary biliary cirrhosis or primary biliary cholangitis as the diagnosis. Apply it for confirmed chronic autoimmune bile duct disease, including cases described as early or established cirrhosis. Do not infer the diagnosis from abnormal liver tests alone; check documentation.
Do not use for
Do not use this code for other causes of cirrhosis, hepatitis, or nonspecific cholestasis. If the record only says “liver disease” or “elevated liver enzymes,” check documentation.
Coding tip
Code only when the provider clearly links the condition to primary biliary disease, and follow any documented terminology changes such as “primary biliary cholangitis.”