ICD-10 Code H53.51 – Achromatopsia (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H53.51 – Achromatopsia
What it is
Achromatopsia is a rare inherited vision disorder marked by absent or severely reduced color vision. It usually affects how the eyes respond to light and can cause poor visual clarity.
Clinical signs
Typical findings include very limited color discrimination, light sensitivity, reduced visual acuity, and involuntary eye movements. Clinical features vary; refer to documentation.
When to use this code
Use H53.51 when the provider documents achromatopsia, complete color blindness, or congenital color vision loss consistent with this diagnosis. Code it from the record when the condition is the reason for evaluation or a confirmed active diagnosis. Check documentation if the note only says “color vision problem.”
Do not use for
Do not use this code for acquired color vision changes, nonspecific visual disturbance, or suspected color blindness without confirmation. If the documentation does not clearly support achromatopsia, check documentation.
Coding tip
Confirm that the provider specifically names achromatopsia, because general color blindness terms may require a different code.