ICD-10 Code H35.53 – Other dystrophies primarily involving the sensory retina (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H35.53 – Other dystrophies primarily involving the sensory retina
What it is
This code identifies inherited or acquired retinal dystrophic conditions that mainly affect the sensory retina, especially when a more specific retinal dystrophy is not documented. Use it when the record describes a dystrophy but does not name a narrower diagnosis.
Clinical signs
Typical findings may include progressive visual loss, night blindness, reduced peripheral vision, or abnormal retinal appearance on examination. Clinical features vary; refer to documentation.
When to use this code
Use H35.53 when the clinician documents a dystrophy primarily involving the sensory retina and no more specific ICD-10-CM retinal dystrophy code applies. It also fits when the note confirms a retinal dystrophy but the subtype is unspecified or not further defined. Check documentation if the diagnosis is unclear.
Do not use for
Do not use this code for macular degeneration, diabetic retinopathy, or non-dystrophic retinal disorders. If the chart names a specific inherited retinal disease, code that condition instead.
Coding tip
Query for the exact retinal dystrophy subtype before assigning H35.53.