ICD-10 Code H31.21 – Choroideremia (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H31.21 – Choroideremia
What it is
H31.21 identifies choroideremia, an inherited disorder that causes progressive degeneration of the choroid, retinal pigment epithelium, and retina. It is a rare cause of gradual vision loss, usually affecting males more severely.
Clinical signs
Typical findings include night blindness, peripheral visual field loss, and progressive retinal pigment changes on eye examination. Clinical features vary; refer to documentation.
When to use this code
Use H31.21 when the provider documents choroideremia as the confirmed diagnosis. Apply it for ophthalmology notes, genetic evaluations, or follow-up visits describing this inherited retinal degeneration. If the record only mentions hereditary retinal disease without naming choroideremia, check documentation.
Do not use for
Do not use this code for nonspecific retinal degeneration, retinitis pigmentosa, or other hereditary chorioretinal disorders unless choroideremia is specifically documented. Check documentation.
Coding tip
Code only when the diagnosis is stated clearly; if the note says “possible” or “suspected,” query the provider.