ICD-10 Code H18.553 – Macular corneal dystrophy, bilateral (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H18.553 – Macular corneal dystrophy, bilateral
What it is
Macular corneal dystrophy, bilateral is a hereditary corneal disorder that affects both eyes. It causes progressive clouding of the cornea from abnormal material buildup.
Clinical signs
Typical findings include bilateral corneal opacity, reduced visual acuity, and scattered stromal haze or spots. Clinical features vary; refer to documentation.
When to use this code
Use this code when the provider documents macular corneal dystrophy affecting both eyes. It is appropriate for confirmed bilateral disease in ophthalmology notes, problem lists, or assessment statements. If the record does not specify laterality, check documentation.
Do not use for
Do not use this code for unilateral macular corneal dystrophy or for nonspecific corneal opacity without a documented dystrophy diagnosis. Do not assume laterality from symptoms alone.
Coding tip
Verify that the documentation explicitly states bilateral involvement before assigning H18.553.