ICD-10 Code H18.53 – Granular corneal dystrophy (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H18.53 – Granular corneal dystrophy
What it is
H18.53 identifies granular corneal dystrophy, an inherited corneal disorder in which small, crumb-like opacities develop in the corneal stroma. It usually affects both eyes and can gradually reduce vision.
Clinical signs
Typical findings include discrete white or gray corneal deposits with a granular appearance, often seen on slit-lamp examination. Clinical features vary; refer to documentation if the subtype or corneal layer involvement is unclear.
When to use this code
Use this code when the provider documents granular corneal dystrophy, including routine ophthalmology follow-up for known disease. It is also appropriate when the diagnosis is confirmed by exam findings and the note specifically names this dystrophy. If the record only says corneal opacity, check documentation before coding.
Do not use for
Do not use H18.53 for corneal scars, infectious keratitis, or nonspecific corneal opacity without a documented granular dystrophy diagnosis. Check documentation when the condition is described only as a family history or suspected disorder.
Coding tip
Code H18.53 only when the clinician documents granular corneal dystrophy by name; otherwise, verify the exact corneal diagnosis in the chart.