ICD-10 Code H18.5 – Hereditary corneal dystrophies (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H18.5 – Hereditary corneal dystrophies
What it is
H18.5 identifies inherited disorders that affect the cornea, the clear front part of the eye. These conditions are usually chronic and may involve one or both eyes.
Clinical signs
Clinical features vary; refer to documentation. Common findings may include corneal opacity, deposits, irregular corneal surface, or reduced vision, depending on the specific dystrophy.
When to use this code
Use H18.5 when the record documents a hereditary corneal dystrophy without a more specific subtype. It is appropriate for confirmed inherited corneal disease affecting the cornea itself. If the provider names a specific dystrophy, code that diagnosis instead.
Do not use for
Do not use this code for acquired corneal scars, infections, or trauma-related corneal changes. Check documentation if the condition is described only as corneal degeneration or opacity without hereditary origin.
Coding tip
Capture the exact subtype when documented, because H18.5 is the broader hereditary corneal dystrophy category.