ICD-10 Code H18.04 – Kayser-Fleischer ring (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code H18.04 – Kayser-Fleischer ring
What it is
H18.04 identifies a Kayser-Fleischer ring, a brownish or greenish ring in the cornea caused by copper deposition. It is most often associated with Wilson disease.
Clinical signs
Typical findings include a visible corneal ring on slit-lamp exam and, in some cases, neurologic or liver-related features of Wilson disease. Clinical features vary; refer to documentation.
When to use this code
Use H18.04 when the provider documents a Kayser-Fleischer ring, whether found on exam or noted as part of an eye evaluation. You may also use it when the ring is documented during workup for Wilson disease. Do not assume the diagnosis without explicit documentation.
Do not use for
Do not use this code for general corneal discoloration, other corneal deposits, or suspected Wilson disease without a documented Kayser-Fleischer ring. Check documentation.
Coding tip
Code the ring only when it is specifically documented; if the record mentions Wilson disease alone, select the disease code instead.