ICD-10 Code G93.44 – Adult-onset leukodystrophy with axonal spheroids (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G93.44 – Adult-onset leukodystrophy with axonal spheroids
What it is
This code identifies adult-onset leukodystrophy with axonal spheroids, a rare inherited white-matter disorder that affects the brain’s myelin and nerve fibers. Use it when documentation names this specific diagnosis.
Clinical signs
Clinical features vary; refer to documentation. Commonly reported findings include progressive neurologic decline, cognitive or psychiatric changes, gait disturbance, and other signs of central nervous system white-matter disease.
When to use this code
Use G93.44 when the provider documents adult-onset leukodystrophy with axonal spheroids as the confirmed diagnosis. It may appear in neurology or genetics records after imaging, family history review, or specialist evaluation.
Code it for established cases, not for a vague concern about leukodystrophy. If the record only says “white-matter changes” or “demyelinating disease,” check documentation for the exact condition.
Do not use for
Do not use this code for other leukodystrophies, nonspecific encephalopathy, or demyelinating disorders without this exact diagnosis. Check documentation if the condition is suspected but not confirmed.
Coding tip
Match the code to the exact named disorder in the assessment, not to imaging findings alone.