ICD-10 Code G71.22 – Centronuclear myopathy (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G71.22 – Centronuclear myopathy
What it is
G71.22 identifies centronuclear myopathy, a rare inherited muscle disorder in which muscle fibers have centrally placed nuclei. Use it for the specific diagnosis documented by the provider.
Clinical signs
Clinical features vary; refer to documentation. Common findings include hypotonia, muscle weakness, delayed motor milestones, and sometimes respiratory involvement or facial weakness.
When to use this code
Use this code when the record clearly states centronuclear myopathy or a synonymous confirmed diagnosis. It is appropriate for outpatient, inpatient, or problem-list documentation when the condition is being evaluated, monitored, or managed.
If the chart only says “myopathy” or lists weakness without a named subtype, check documentation before assigning G71.22. Do not infer this diagnosis from nonspecific neuromuscular symptoms alone.
Do not use for
Do not use G71.22 for other inherited myopathies, muscular dystrophies, or unspecified muscle weakness. If the provider documents a different neuromuscular disorder, code that condition instead.
Coding tip
Code G71.22 only when the subtype is explicitly documented; otherwise, query for clarification.