ICD-10 Code G71.2 – Congenital Myopathies (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G71.2 – Congenital myopathies
What it is
G71.2 identifies congenital myopathies, a group of inherited muscle disorders present at birth or early childhood. They cause weakness from abnormal muscle structure rather than nerve disease.
Clinical signs
Typical findings include hypotonia, delayed motor milestones, and generalized muscle weakness. Clinical features vary; refer to documentation for the specific congenital myopathy subtype and any biopsy or genetic confirmation.
When to use this code
Use G71.2 when the provider documents congenital myopathy, congenital muscle disease, or a named congenital myopathy subtype. It is appropriate when the diagnosis is established or clearly supported in the record. If the note only says “muscle weakness,” check documentation before coding.
Do not use for
Do not use this code for acquired myopathies, muscular dystrophies, or nonspecific weakness without a congenital myopathy diagnosis. Check documentation if the condition is still under evaluation.
Coding tip
Code the documented congenital myopathy subtype when specified; otherwise use G71.2 only when the record clearly supports a congenital myopathy diagnosis.