ICD-10 Code G40.C09 – Lafora progressive myoclonus epilepsy, not intractable, without status epilepticus (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G40.C09 – Lafora progressive myoclonus epilepsy, not intractable, without status epilepticus
What it is
This code identifies Lafora progressive myoclonus epilepsy, a rare inherited epilepsy with progressive neurologic decline. Use it when the diagnosis is documented and the seizures are not described as intractable and there is no status epilepticus.
Clinical signs
Typical findings include myoclonic jerks, generalized seizures, and worsening neurologic function over time. Clinical features vary; refer to documentation for the specific seizure pattern and any associated cognitive decline.
When to use this code
Use this code when the record specifically names Lafora progressive myoclonus epilepsy and indicates the seizures are not intractable. It also applies when there is no documentation of status epilepticus. If the note is incomplete, check documentation before assigning the code.
Do not use for
Do not use this code if the epilepsy is documented as intractable or if status epilepticus is present. Do not use it for other myoclonic epilepsies unless Lafora disease is clearly stated.
Coding tip
Confirm both the Lafora diagnosis and the absence of intractability or status epilepticus in the provider note before coding.