ICD-10 Code G40.B1 – Juvenile myoclonic epilepsy, intractable (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G40.B1 – Juvenile myoclonic epilepsy, intractable
What it is
Use this code for juvenile myoclonic epilepsy that is not controlled by standard therapy. It identifies a chronic seizure disorder beginning in adolescence, with persistent seizures despite treatment.
Clinical signs
Typical findings include myoclonic jerks, often on awakening, and may also include generalized tonic-clonic seizures. Clinical features vary; refer to documentation for seizure type and whether the epilepsy is truly intractable.
When to use this code
Assign G40.B1 when the provider documents juvenile myoclonic epilepsy and states it is intractable, refractory, or poorly controlled. Use it when the record supports ongoing seizures despite appropriate antiseizure management. Check documentation if the note does not clearly confirm intractability.
Do not use for
Do not use this code for juvenile myoclonic epilepsy without intractability; a different ICD-10-CM code applies. Do not use it when the seizure disorder is unspecified or when documentation only says “history of seizures.”
Coding tip
Confirm both the epilepsy type and the intractable status in the provider’s assessment before coding.