ICD-10 Code G40.401 – Other generalized epilepsy and epileptic syndromes, not intractable, with status epilepticus (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code G40.401 – Other generalized epilepsy and epileptic syndromes, not intractable, with status epilepticus
What it is
This code identifies a generalized epilepsy or epileptic syndrome with status epilepticus, and the seizures are not described as intractable. Use it when the record shows prolonged or recurrent seizure activity in a generalized epilepsy pattern.
Clinical signs
Clinical features vary; refer to documentation. Status epilepticus typically means ongoing seizure activity or repeated seizures without return to baseline, and the epilepsy is documented as generalized rather than focal.
When to use this code
Use this code when the provider documents a generalized epilepsy syndrome with status epilepticus and does not describe the condition as intractable. It may apply during emergency care, inpatient admission, or follow-up notes that clearly confirm the episode.
Code it only when the record links the status epilepticus to the generalized epilepsy diagnosis. Check documentation if seizure type, chronicity, or intractability is unclear.
Do not use for
Do not use this code for focal epilepsy, absence of status epilepticus, or seizures not documented as part of an epileptic syndrome. Do not assume intractability unless the provider states it.
Coding tip
Verify both elements in the chart: generalized epilepsy syndrome and status epilepticus, then confirm that “not intractable” is documented.