ICD-10 Code E83.01 – Wilson’s disease (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E83.01 – Wilson’s disease
What it is
E83.01 identifies Wilson’s disease, an inherited disorder of copper metabolism. Use it when the record documents copper accumulation affecting the liver, brain, eyes, or other organs.
Clinical signs
Common findings include liver disease, neurologic symptoms, psychiatric changes, and Kayser-Fleischer rings. Clinical features vary; refer to documentation.
When to use this code
Use E83.01 when the provider diagnoses Wilson’s disease or notes confirmed hereditary copper storage disorder. It may appear in hepatology, neurology, or genetics records when the condition is the reason for evaluation or ongoing management.
Code it from clear documentation rather than suspicion alone. If the chart only mentions abnormal liver tests or family history without a diagnosis, check documentation before assigning this code.
Do not use for
Do not use this code for nonspecific copper deficiency, general liver disease, or abnormal laboratory findings without Wilson’s disease documented. Check documentation.
Coding tip
Verify that the provider states Wilson’s disease explicitly; family history or screening alone is not enough.