ICD-10 Code E75.5 – Other lipid storage disorders (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E75.5 – Other lipid storage disorders
What it is
E75.5 identifies lipid storage disorders that do not fit a more specific inherited disorder code. These conditions involve abnormal buildup or handling of lipids in the body.
Clinical signs
Clinical features vary; refer to documentation. Common findings may include organ enlargement, neurologic involvement, or signs of progressive metabolic disease, depending on the specific disorder.
When to use this code
Use E75.5 when the record documents a lipid storage disorder but does not name a more specific diagnosis. It is also appropriate when the clinician describes an atypical or unspecified lipid storage condition. Code the documented disorder as written and avoid assuming a subtype.
Do not use for
Do not use this code for a clearly identified lipid storage disease with its own specific ICD-10-CM code. Check documentation if the chart only mentions hyperlipidemia, cholesterol disorder, or another non-storage lipid condition.
Coding tip
Choose the most specific lipid storage diagnosis documented; if the exact disorder is unclear, E75.5 may be the best match.