ICD-10 Code E40 – Kwashiorkor (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E40 – Kwashiorkor
What it is
Kwashiorkor is a severe form of protein-energy malnutrition, usually linked to inadequate protein intake. It is a serious diagnosis that reflects nutritional deficiency, not a specific organ disease.
Clinical signs
Typical findings include edema, abdominal distention, muscle wasting, and skin or hair changes. Clinical features vary; refer to documentation.
When to use this code
Use E40 when the provider documents kwashiorkor or severe protein malnutrition consistent with this diagnosis. It may appear in patients with marked nutritional deficiency and edema. Code only when the record clearly supports kwashiorkor rather than another malnutrition type.
Do not use for
Do not use this code for simple underweight, unspecified malnutrition, or marasmus unless kwashiorkor is documented. Check documentation if the chart uses vague terms such as “poor nutrition.”
Coding tip
Assign E40 only when the note specifically supports kwashiorkor; otherwise query for clarification.