ICD-10 Code E26.02 – Glucocorticoid-remediable aldosteronism (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E26.02 – Glucocorticoid-remediable aldosteronism
What it is
Glucocorticoid-remediable aldosteronism is a hereditary form of primary aldosteronism. It causes excess aldosterone production that can improve with glucocorticoid therapy.
Clinical signs
Patients may have hypertension, low potassium, or a family history of early-onset high blood pressure. Clinical features vary; refer to documentation.
When to use this code
Use this code when the provider documents glucocorticoid-remediable aldosteronism, familial hyperaldosteronism type I, or an equivalent confirmed diagnosis. It is appropriate when the record identifies the condition as the cause of primary aldosteronism. Check documentation if the note only says suspected hyperaldosteronism.
Do not use for
Do not use this code for other causes of primary aldosteronism, such as adrenal adenoma or bilateral adrenal hyperplasia. Do not assign it for nonspecific hypertension without documented glucocorticoid-remediable aldosteronism.
Coding tip
Look for explicit family history or genetic confirmation in the chart, because the diagnosis is often documented under familial hyperaldosteronism.