ICD-10 Code E20.1 – Pseudohypoparathyroidism (2026): Diagnosis, Symptoms & Billing Guide
2026 ICD-10-CM Diagnosis Code E20.1 – Pseudohypoparathyroidism
What it is
Pseudohypoparathyroidism is a disorder in which the body does not respond normally to parathyroid hormone. This can cause low calcium and related metabolic changes despite adequate hormone production.
Clinical signs
Typical findings include signs of hypocalcemia and, in some patients, features of Albright hereditary osteodystrophy. Clinical features vary; refer to documentation.
When to use this code
Use E20.1 when the provider documents pseudohypoparathyroidism or an established diagnosis of parathyroid hormone resistance. It is appropriate when the record supports the condition, even if the note emphasizes associated calcium or phosphate abnormalities. Check documentation if the diagnosis is uncertain.
Do not use for
Do not use this code for simple hypocalcemia, hypoparathyroidism, or other calcium disorders without documented pseudohypoparathyroidism. If the chart only says “low calcium,” code the documented condition instead.
Coding tip
Look for explicit mention of hormone resistance or pseudohypoparathyroidism in the assessment, not just abnormal labs.